From: Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases
Age | 23 m–56 y (median, 23 y) | |
 < 10 y | 4 (11%) | |
10–19 y | 13 (38%) | |
 ≥ 20 y | 18 (51%) | |
Gender | Male | 10 (29%) |
Female | 25 (71%) | |
Symptoms | Perianal mass | 34 (97%) |
Pain | 20 (57%) | |
Inguinal mass | 2 (6%) | |
Bloody stool | 2 (6%) | |
Difficult defecation | 2 (6%) | |
Fecal incontinence | 1 (3%) | |
Misdiagnosis history/time interval of diagnosis |  | 35 (3 d–10 m, 3.1 m) |
Misdiagnosis | 16 (10 d–3 m, 2.6 m) | |
No misdiagnosis | 19 (3 d–10 m, 3.4 m) | |
Pathological subtype | Alveolar | 9 |
Embryonal | 14 | |
Pleomorphic | 1 | |
ND | 11 | |
IRS clinical group | I | 1 |
II | 11 | |
III | 8 | |
IV | 5 | |
ND | 10 | |
Stage | 2 | 6 |
3 | 15 | |
4 | 5 | |
ND | 9 | |
Tumor site | Perianal | 26 |
Perineal | 9 | |
Tumor size |  < 5 cm | 12 |
 ≥ 5 cm | 22 | |
ND | 1 | |
Regional lymph node metastasis | N0 | 7 |
N1 | 15 | |
ND | 13 | |
Distant metastasis | M0 | 17 |
M1 | 5 | |
ND | 12 | |
Surgical approach | LRR | 12 |
APR | 7 | |
No surgery or biopsy only | 9 | |
ND | 7 | |
Outcome | Survival time < 5 y | 5 |
NED | 3 | |
AWD | 2 | |
Survival time ≥ 5 y | 3 | |
NED | 2 | |
AWD | 1 | |
DOD | 14 | |
ND | 13 |