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Table 1 Summary of reports of IPH requiring liver transplantation

From: Living donor liver transplantation for idiopathic portal hypertension with extrahepatic portal vein stenosis and splenic artery aneurysms: a case report and review of the literature

Authors Year Patients no Gender Diagnosis before LT LT Pathological diagnosis Prognosis
McDonald et al. [14] 1990 1 Male Cirrhosis OLT NRH Died (4 months)
Elariny et al. [15] 1994 1 Female Cirrhosis OLT NRH Alive
Bernard et al. [16] 1995 1 Male Cirrhosis OLT ISC Alive
Loinaz et al. [17] 1998 4 Male 4 NRH 1, cirrhosis 1, nodular liver 1, chronic liver disease 1 OLT NRH 3, partial nodular transformation 1 Alive 2, died 2 (1 month, 3 months)
Radomski et al. [18] 2000 4 Male 3
Female 1
Cirrhosis 4 OLT NRH 4 Alive 4
Dumortier et al. [19] 2001 8 Male 8 IPH 8 OLT NRH 3, ISC 5 Alive 8
Krasinskas et al. [3] 2005 16 Male 11
Female 5
Cirrhosis 13, NCPH related 3 OLT Portal vascular abnormalities 16, NRH 15, ISC 9 Alive 14, died 1 (5 months), retransplantation 1
Inokuma et al. [5] 2009 1 Female IPH LDLT Portal vascular abnormalities Died (5 months)
Saigai et al. [20] 2011 10 Male 8
Female 2
Cryptogenic cirrhosis 9, alcoholic cirrhosis 1 LDLT Pure NCPF Unknown 10
Matsumoto et al. [9] 2013 1 Male Cryptogenic cirrhosis, atrophied portal venous trunk LDLT, renoportal anastomosis IPH Alive
Our case 2020 1 Female IPH, extrahepatic portal vein stenosis LDLT, interposition SFV graft IPH Alive
Total   48 Male 38
Female 10
Extrahepatic portal vein abnormalities 2 OLT 35
LDLT 13
  Died 5, alive 33, unknown 10
  1. LT liver transplantation, OLT orthotopic liver transplantation, LDLT living donor liver transplantation, NRH nodular regenerative hyperplasia, ISC incomplete septal cirrhosis, IPH idiopathic portal hypertension